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Regulation of CFTR Biogenesis by the Proteostatic Network and Pharmacological Modulators

Cystic fibrosis (CF) is the most common lethal inherited disease among Caucasians in North America and a significant portion of Europe. The disease arises from one of many mutations in the gene encoding the cystic fibrosis transmembrane conductance regulator, or CFTR. The most common disease-associa...

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Detalhes bibliográficos
Publicado no:Int J Mol Sci
Main Authors: Estabrooks, Samuel, Brodsky, Jeffrey L.
Formato: Artigo
Idioma:Inglês
Publicado em: MDPI 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7013518/
https://ncbi.nlm.nih.gov/pubmed/31936842
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms21020452
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