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Molecular Mechanisms and Therapeutics for the GAA·TTC Expansion Disease Friedreich Ataxia

Friedreich ataxia (FRDA), the most common inherited ataxia, is caused by transcriptional silencing of the nuclear FXN gene, encoding the essential mitochondrial protein frataxin. Currently, there is no approved therapy for this fatal disorder. Gene silencing in FRDA is due to hyperexpansion of the t...

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Bibliographic Details
Published in:Neurotherapeutics
Main Author: Gottesfeld, Joel M.
Format: Artigo
Language:Inglês
Published: Springer International Publishing 2019
Subjects:
Online Access:https://ncbi.nlm.nih.gov/pmc/articles/PMC6985418/
https://ncbi.nlm.nih.gov/pubmed/31317428
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s13311-019-00764-x
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