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Epidermolysis Bullosa-Associated Squamous Cell Carcinoma: From Pathogenesis to Therapeutic Perspectives

Epidermolysis bullosa (EB) is a heterogeneous group of inherited skin disorders determined by mutations in genes encoding for structural components of the cutaneous basement membrane zone. Disease hallmarks are skin fragility and unremitting blistering. The most disabling EB (sub)types show defectiv...

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Библиографические подробности
Опубликовано в: :Int J Mol Sci
Главные авторы: Condorelli, Angelo Giuseppe, Dellambra, Elena, Logli, Elena, Zambruno, Giovanna, Castiglia, Daniele
Формат: Artigo
Язык:Inglês
Опубликовано: MDPI 2019
Предметы:
Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC6888002/
https://ncbi.nlm.nih.gov/pubmed/31739489
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms20225707
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