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Epidermolysis Bullosa-Associated Squamous Cell Carcinoma: From Pathogenesis to Therapeutic Perspectives

Epidermolysis bullosa (EB) is a heterogeneous group of inherited skin disorders determined by mutations in genes encoding for structural components of the cutaneous basement membrane zone. Disease hallmarks are skin fragility and unremitting blistering. The most disabling EB (sub)types show defectiv...

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Detalhes bibliográficos
Publicado no:Int J Mol Sci
Main Authors: Condorelli, Angelo Giuseppe, Dellambra, Elena, Logli, Elena, Zambruno, Giovanna, Castiglia, Daniele
Formato: Artigo
Idioma:Inglês
Publicado em: MDPI 2019
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6888002/
https://ncbi.nlm.nih.gov/pubmed/31739489
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms20225707
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