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Epidermolysis Bullosa-Associated Squamous Cell Carcinoma: From Pathogenesis to Therapeutic Perspectives

Epidermolysis bullosa (EB) is a heterogeneous group of inherited skin disorders determined by mutations in genes encoding for structural components of the cutaneous basement membrane zone. Disease hallmarks are skin fragility and unremitting blistering. The most disabling EB (sub)types show defectiv...

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Podrobná bibliografie
Vydáno v:Int J Mol Sci
Hlavní autoři: Condorelli, Angelo Giuseppe, Dellambra, Elena, Logli, Elena, Zambruno, Giovanna, Castiglia, Daniele
Médium: Artigo
Jazyk:Inglês
Vydáno: MDPI 2019
Témata:
On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC6888002/
https://ncbi.nlm.nih.gov/pubmed/31739489
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms20225707
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