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Pathogenic mutations in genes encoding nuclear envelope proteins and defective nucleocytoplasmic connections

Mutations in genes encoding nuclear lamins and associated nuclear envelope proteins have been linked to a broad range of inherited diseases affecting different tissues and organs. These diseases are often referred to as laminopathies. Scientists have yet to elucidate exactly how pathogenic mutations...

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Bibliografski detalji
Izdano u:Exp Biol Med (Maywood)
Glavni autori: Östlund, Cecilia, Chang, Wakam, Gundersen, Gregg G, Worman, Howard J
Format: Artigo
Jezik:Inglês
Izdano: SAGE Publications 2019
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC6880145/
https://ncbi.nlm.nih.gov/pubmed/31299860
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1177/1535370219862243
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