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Lowering the culture temperature corrects collagen abnormalities caused by HSP47 gene knockout

Heat shock protein 47 (HSP47) is an endoplasmic reticulum (ER)-resident molecular chaperone that specifically recognizes triple helical portions of procollagens. The chaperone function of HSP47 is indispensable in mammals, and hsp47-null mice show an embryonic lethal phenotype accompanied by severe...

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Detalhes bibliográficos
Publicado no:Sci Rep
Main Authors: Fujii, Kazunori K., Taga, Yuki, Sakai, Takayuki, Ito, Shinya, Hattori, Shunji, Nagata, Kazuhiro, Koide, Takaki
Formato: Artigo
Idioma:Inglês
Publicado em: Nature Publishing Group UK 2019
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6874656/
https://ncbi.nlm.nih.gov/pubmed/31758055
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s41598-019-53962-0
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