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Atypical reduction of plasma ADAMTS13 activity by a non-IgG-type inhibitor in a patient with hemolytic uremic syndrome caused by Shiga toxin-producing Escherichia coli

Thrombotic microangiopathies include hemolytic uremic syndrome (HUS) and thrombotic thrombocytopenic purpura (TTP). Measurement of plasma levels of “a disintegrin-like and metalloproteinase with thrombospondin type 1 motifs 13” (ADAMTS13) activity can distinguish HUS from TTP. Reduced plasma ADAMTS1...

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Detalhes bibliográficos
Publicado no:CEN Case Rep
Main Authors: Nakayama, Shinya, Hirashio, Shuma, Yorishima, Haruka, Doi, Toshiki, Yoshida, Yoko, Matsumoto, Masanori, Masaki, Takao
Formato: Artigo
Idioma:Inglês
Publicado em: Springer Singapore 2019
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6820649/
https://ncbi.nlm.nih.gov/pubmed/31177384
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s13730-019-00405-4
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