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Acute Recurrent and Chronic Pancreatitis as Initial Manifestations of Cystic Fibrosis and Cystic Fibrosis Transmembrane Conductance Regulator-Related Disorders

OBJECTIVES: Recurrent pancreatitis is considered a rare manifestation of cystic fibrosis transmembrane conductance regulator (CFTR) dysfunction; this case series highlights that pancreatitis can be a presenting symptoms of cystic fibrosis (CF) or a CFTR-related disorder (CFTR-RD). METHODS: Retrospec...

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Publicat a:Pancreas
Autors principals: Baldwin, Christina, Zerofsky, Melissa, Sathe, Meghana, Troendle, David M., Perito, Emily R.
Format: Artigo
Idioma:Inglês
Publicat: 2019
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6768061/
https://ncbi.nlm.nih.gov/pubmed/31268981
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/MPA.0000000000001350
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