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Mechanisms of exercise‐induced survival motor neuron expression in the skeletal muscle of spinal muscular atrophy‐like mice

KEY POINTS: Spinal muscular atrophy (SMA) is a health‐ and life‐limiting neuromuscular disorder caused by a deficiency in survival motor neuron (SMN) protein. While historically considered a motor neuron disease, current understanding of SMA emphasizes its systemic nature, which requires addressing...

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Pubblicato in:J Physiol
Autori principali: Ng, Sean Y., Mikhail, Andrew, Ljubicic, Vladimir
Natura: Artigo
Lingua:Inglês
Pubblicazione: John Wiley and Sons Inc. 2019
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6767691/
https://ncbi.nlm.nih.gov/pubmed/31361024
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1113/JP278454
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