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Hemophagocytic lymphohistiocytosis of indeterminate cause: a fatal adult case
Hemophagocytic lymphohistiocytosis (HLH) is an uncommon life-threatening disorder characterized by wide spread non-neoplastic proliferation and inappropriate activation of mature macrophages resulting in hypercytokinemia. This uncontrollable and ineffective systemic immune response causes fever, hep...
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| Vydáno v: | Autops Case Rep |
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| Hlavní autoři: | , , , , , , |
| Médium: | Artigo |
| Jazyk: | Inglês |
| Vydáno: |
São Paulo, SP: Universidade de São Paulo, Hospital Universitário
2012
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| Témata: | |
| On-line přístup: | https://ncbi.nlm.nih.gov/pmc/articles/PMC6735545/ https://ncbi.nlm.nih.gov/pubmed/31528566 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4322/acr.2012.011 |
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