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Hemophagocytic lymphohistiocytosis of indeterminate cause: a fatal adult case
Hemophagocytic lymphohistiocytosis (HLH) is an uncommon life-threatening disorder characterized by wide spread non-neoplastic proliferation and inappropriate activation of mature macrophages resulting in hypercytokinemia. This uncontrollable and ineffective systemic immune response causes fever, hep...
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| Publicado no: | Autopsy and Case Reports |
|---|---|
| Main Authors: | , , , , , , |
| Formato: | Artigo |
| Idioma: | Inglês |
| Publicado em: |
Hospital Universitário da Universidade de São Paulo
2012
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| Assuntos: | |
| Acesso em linha: | https://www.redalyc.org/articulo.oa?id=576060814005 |
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