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Hemophagocytic lymphohistiocytosis of indeterminate cause: a fatal adult case

Hemophagocytic lymphohistiocytosis (HLH) is an uncommon life-threatening disorder characterized by wide spread non-neoplastic proliferation and inappropriate activation of mature macrophages resulting in hypercytokinemia. This uncontrollable and ineffective systemic immune response causes fever, hep...

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Detalles Bibliográficos
Publicado en:Autops Case Rep
Autores principales: de Campos, Fernando Peixoto Ferraz, de Lima, Patrícia Picciarelli, Lima, Fabiana Roberto, Simões, Angélica Braz, Kim, Elizabeth In Myung, Smeili, Luciana Andréa Avena, Zerbini, Maria Claudia Nogueira
Formato: Artigo
Lenguaje:Inglês
Publicado: São Paulo, SP: Universidade de São Paulo, Hospital Universitário 2012
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC6735545/
https://ncbi.nlm.nih.gov/pubmed/31528566
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4322/acr.2012.011
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