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Translation of the quality-of-life measure for adults with primary ciliary dyskinesia and its application in patients in Brazil

Primary ciliary dyskinesia (PCD) is a genetic disorder that is typically inherited in an autosomal recessive manner. It is clinically characterized by recurrent respiratory infections. However, its repercussions for patient quality of life should not be overlooked. Studies have shown that PCD has a...

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Enregistré dans:
Détails bibliographiques
Publié dans:J Bras Pneumol
Auteurs principaux: de Queiroz, Ana Paula Lima, Athanazio, Rodrigo Abensur, Olm, Mary Anne Kowal, Rubbo, Bruna, Casal, Yuri Reis, Lucas, Jane, Behan, Laura
Format: Artigo
Langue:Inglês
Publié: Sociedade Brasileira de Pneumologia e Tisiologia 2019
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC6715036/
https://ncbi.nlm.nih.gov/pubmed/31038545
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1590/1806-3713/e20170358
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