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Translation of the quality-of-life measure for adults with primary ciliary dyskinesia and its application in patients in Brazil

Primary ciliary dyskinesia (PCD) is a genetic disorder that is typically inherited in an autosomal recessive manner. It is clinically characterized by recurrent respiratory infections. However, its repercussions for patient quality of life should not be overlooked. Studies have shown that PCD has a...

詳細記述

保存先:
書誌詳細
出版年:J Bras Pneumol
主要な著者: de Queiroz, Ana Paula Lima, Athanazio, Rodrigo Abensur, Olm, Mary Anne Kowal, Rubbo, Bruna, Casal, Yuri Reis, Lucas, Jane, Behan, Laura
フォーマット: Artigo
言語:Inglês
出版事項: Sociedade Brasileira de Pneumologia e Tisiologia 2019
主題:
オンライン・アクセス:https://ncbi.nlm.nih.gov/pmc/articles/PMC6715036/
https://ncbi.nlm.nih.gov/pubmed/31038545
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1590/1806-3713/e20170358
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