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Self-efficacy and self-management strategies in acute intermittent porphyria

BACKGROUND: Acute intermittent porphyria (AIP) is an inherited metabolic disease with low clinical penetrance caused by mutations in the hydroxymethylbilane (HMBS) gene. Although most patients experience little or no symptoms, serious attacks may include excruciating pain, severe electrolyte disturb...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:BMC Health Serv Res
Egile Nagusiak: Hammersland, Marte H., Aarsand, Aasne K., Sandberg, Sverre, Andersen, Janice
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: BioMed Central 2019
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC6607542/
https://ncbi.nlm.nih.gov/pubmed/31269991
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s12913-019-4285-9
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