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Self-efficacy and self-management strategies in acute intermittent porphyria

BACKGROUND: Acute intermittent porphyria (AIP) is an inherited metabolic disease with low clinical penetrance caused by mutations in the hydroxymethylbilane (HMBS) gene. Although most patients experience little or no symptoms, serious attacks may include excruciating pain, severe electrolyte disturb...

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Pubblicato in:BMC Health Serv Res
Autori principali: Hammersland, Marte H., Aarsand, Aasne K., Sandberg, Sverre, Andersen, Janice
Natura: Artigo
Lingua:Inglês
Pubblicazione: BioMed Central 2019
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6607542/
https://ncbi.nlm.nih.gov/pubmed/31269991
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s12913-019-4285-9
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