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Current challenges in the management of patients with sickle cell disease – A report of the Italian experience

Sickle cell disease (SCD) is an inherited red blood cell disorder caused by a structural abnormality of hemoglobin called sickle hemoglobin (HbS). Clinical manifestations of SCD are mainly characterized by chronic hemolysis and acute vaso-occlusive crisis, which are responsible for severe acute and...

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Detaylı Bibliyografya
Yayımlandı:Orphanet J Rare Dis
Asıl Yazarlar: Russo, Giovanna, De Franceschi, Lucia, Colombatti, Raffaella, Rigano, Paolo, Perrotta, Silverio, Voi, Vincenzo, Palazzi, Giovanni, Fidone, Carmelo, Quota, Alessandra, Graziadei, Giovanna, Pietrangelo, Antonello, Pinto, Valeria, Ruffo, Giovan Battista, Sorrentino, Francesco, Venturelli, Donatella, Casale, Maddalena, Ferrara, Francesca, Sainati, Laura, Cappellini, Maria Domenica, Piga, Antonio, Maggio, Aurelio, Forni, Gian Luca
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: BioMed Central 2019
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC6543611/
https://ncbi.nlm.nih.gov/pubmed/31146777
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13023-019-1099-0
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