Carregant...

A bone mineralization defect in the Pah(enu2) model of classical phenylketonuria involves compromised mesenchymal stem cell differentiation

Osteopenia is observed in some patients affected by phenylalanine hydroxylase (PAH) deficient phenylketonuria (PKU). Bone density studies, in diverse PKU patient cohorts, have demonstrated bone disease is neither fully penetrant nor uniform in bone density loss. Biochemical assessment has generated...

Descripció completa

Guardat en:
Dades bibliogràfiques
Publicat a:Mol Genet Metab
Autors principals: Dobrowolski, Steven F., Tourkova, Irina L., Robinson, Lisa J., Secunda, Cassandra, Spridik, Kayla, Blair, Harry C.
Format: Artigo
Idioma:Inglês
Publicat: 2018
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6542264/
https://ncbi.nlm.nih.gov/pubmed/30201326
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.ymgme.2018.08.010
Etiquetes: Afegir etiqueta
Sense etiquetes, Sigues el primer a etiquetar aquest registre!