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Fibrous Dysplasia of Bone and McCune-Albright Syndrome: a Bench to Bedside Review

Fibrous dysplasia is an uncommon mosaic disorder in which bone is replaced by structurally unsound fibro-osseous tissue. It is caused by the sporadic post-zygotic activating mutations in GNAS, resulting in dysregulated Gα(S)-protein signaling in affected tissues. This manifests on a broad clinical s...

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Vydáno v:Calcif Tissue Int
Hlavní autoři: Hartley, Iris, Zhadina, Maria, Collins, Micheal T, Boyce, Alison M
Médium: Artigo
Jazyk:Inglês
Vydáno: 2019
Témata:
On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC6541017/
https://ncbi.nlm.nih.gov/pubmed/31037426
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s00223-019-00550-z
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