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Fibrous dysplasia/McCune-Albright Syndrome: Clinical and Translational Perspectives

Fibrous dysplasia (FD) is an uncommon and debilitating skeletal disorder resulting in fractures, deformity, functional impairment and pain. It arises from postzygotic somatic activating mutations in GNAS, in the cAMP-regulating transcript α-subunit, G(s)α. Constitutive G(s) signaling results in acti...

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Bibliografiska uppgifter
I publikationen:Curr Osteoporos Rep
Huvudupphovsmän: Robinson, Cemre, Collins, Michael T, Boyce, Alison M
Materialtyp: Artigo
Språk:Inglês
Publicerad: 2016
Ämnen:
Länkar:https://ncbi.nlm.nih.gov/pmc/articles/PMC5035212/
https://ncbi.nlm.nih.gov/pubmed/27492469
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s11914-016-0317-0
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