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Restoration of correct β(IVS2-654)-globin mRNA splicing and HbA production by engineered U7 snRNA in β-thalassaemia/HbE erythroid cells

A cytosine to thymine mutation at nucleotide 654 of human β-globin intron 2 (β(IVS2-654)) is one of the most common mutations causing β-thalassaemia in Chinese and Southeast Asians. This mutation results in aberrant β-globin pre-mRNA splicing and prevents synthesis of β-globin protein. Splicing corr...

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Publicado en:Sci Rep
Autores principales: Nualkaew, Tiwaporn, Jearawiriyapaisarn, Natee, Hongeng, Suradej, Fucharoen, Suthat, Kole, Ryszard, Svasti, Saovaros
Formato: Artigo
Lenguaje:Inglês
Publicado: Nature Publishing Group UK 2019
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC6529457/
https://ncbi.nlm.nih.gov/pubmed/31113996
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s41598-019-43964-3
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