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Absence of BBSome function leads to astrocyte reactivity in the brain

In humans, dysfunctional primary cilia result in Bardet-Biedl syndrome (BBS), which presents with clinical features including intellectual disabilities, obesity, and retinal degeneration, and, in mouse models, the added feature of hydrocephalus. We observed increased Glial Fibrillary Acidic Protein...

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Détails bibliographiques
Publié dans:Mol Brain
Auteurs principaux: Singh, Minati, Garrison, Janelle E., Wang, Kai, Sheffield, Val C.
Format: Artigo
Langue:Inglês
Publié: BioMed Central 2019
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC6509862/
https://ncbi.nlm.nih.gov/pubmed/31072410
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13041-019-0466-z
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