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GRP75 overexpression rescues frataxin deficiency and mitochondrial phenotypes in Friedreich ataxia cellular models

Friedreich ataxia (FRDA) is an autosomal recessive neurodegenerative disease caused by the deficiency of frataxin, a mitochondrial protein crucial for iron–sulfur cluster biogenesis and adenosine triphosphate (ATP) production. Currently, there is no therapy to slow down the progression of FRDA. Rece...

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Detalles Bibliográficos
Publicado en:Hum Mol Genet
Main Authors: Dong, Yi Na, McMillan, Emily, Clark, Elisia M, Lin, Hong, Lynch, David R
Formato: Artigo
Idioma:Inglês
Publicado: Oxford University Press 2019
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC6494971/
https://ncbi.nlm.nih.gov/pubmed/30590615
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/hmg/ddy448
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