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Ultrastructure in Transthyretin Amyloidosis: From Pathophysiology to Therapeutic Insights

Transthyretin (TTR) amyloidosis is caused by systemic deposition of wild-type or variant amyloidogenic TTR (ATTRwt and ATTRv, respectively). ATTRwt amyloidosis has traditionally been termed senile systemic amyloidosis, while ATTRv amyloidosis has been called familial amyloid polyneuropathy. Although...

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Vydáno v:Biomedicines
Hlavní autoři: Koike, Haruki, Katsuno, Masahisa
Médium: Artigo
Jazyk:Inglês
Vydáno: MDPI 2019
Témata:
On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC6466231/
https://ncbi.nlm.nih.gov/pubmed/30764529
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/biomedicines7010011
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