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Transthyretin Amyloidosis: Update on the Clinical Spectrum, Pathogenesis, and Disease-Modifying Therapies

ATTR amyloidosis is caused by systemic deposition of transthyretin (TTR) and comprises ATTRwt (wt for wild-type) amyloidosis, ATTRv (v for variant) amyloidosis, and acquired ATTR amyloidosis after domino liver transplantation. ATTRwt amyloidosis has classically been regarded as cardiomyopathy found...

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Detalhes bibliográficos
Publicado no:Neurol Ther
Main Authors: Koike, Haruki, Katsuno, Masahisa
Formato: Artigo
Idioma:Inglês
Publicado em: Springer Healthcare 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7500251/
https://ncbi.nlm.nih.gov/pubmed/32948978
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s40120-020-00210-7
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