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Widespread Cardiac and Vasomotor Autonomic Dysfunction in Non-Val30Met Hereditary Transthyretin Amyloidosis

OBJECTIVE: The autonomic functions of hereditary transthyretin (ATTRm) amyloidosis, traditionally referred to as familial amyloid polyneuropathy, have primarily been investigated in patients with Val30Met mutations, and information regarding non-Val30Met patients is scarce. The aim of this study was...

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Detalhes bibliográficos
Publicado no:Intern Med
Principais autores: Koike, Haruki, Nakamura, Tomohiko, Nishi, Ryoji, Ikeda, Shohei, Kawagashira, Yuichi, Iijima, Masahiro, Katsuno, Masahisa, Sobue, Gen
Formato: Artigo
Idioma:Inglês
Publicado em: The Japanese Society of Internal Medicine 2018
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6306549/
https://ncbi.nlm.nih.gov/pubmed/29984770
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.2169/internalmedicine.1113-18
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