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Impaired Redox Signaling in Huntington’s Disease: Therapeutic Implications

Huntington’s disease (HD) is a neurodegenerative disease triggered by expansion of polyglutamine repeats in the protein huntingtin. Mutant huntingtin (mHtt) aggregates and elicits toxicity by multiple mechanisms which range from dysregulated transcription to disturbances in several metabolic pathway...

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Dettagli Bibliografici
Pubblicato in:Front Mol Neurosci
Autori principali: Paul, Bindu D., Snyder, Solomon H.
Natura: Artigo
Lingua:Inglês
Pubblicazione: Frontiers Media S.A. 2019
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6433839/
https://ncbi.nlm.nih.gov/pubmed/30941013
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fnmol.2019.00068
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