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Impaired Redox Signaling in Huntington’s Disease: Therapeutic Implications

Huntington’s disease (HD) is a neurodegenerative disease triggered by expansion of polyglutamine repeats in the protein huntingtin. Mutant huntingtin (mHtt) aggregates and elicits toxicity by multiple mechanisms which range from dysregulated transcription to disturbances in several metabolic pathway...

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Bibliografske podrobnosti
izdano v:Front Mol Neurosci
Main Authors: Paul, Bindu D., Snyder, Solomon H.
Format: Artigo
Jezik:Inglês
Izdano: Frontiers Media S.A. 2019
Teme:
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC6433839/
https://ncbi.nlm.nih.gov/pubmed/30941013
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fnmol.2019.00068
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