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Absence of LTBP-3 Attenuates the Aneurysmal Phenotype But Not Spinal Effects on the Aorta in Marfan Syndrome

Fibrillin-1 is an elastin-associated glycoprotein that contributes to the long term fatigue resistance of elastic fibers as well as to the bioavailability of transforming growth factor-beta (TGFβ) in arteries. Altered TGFβ bioavailability and/or signaling have been implicated in aneurysm development...

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Detaylı Bibliyografya
Yayımlandı:Biomech Model Mechanobiol
Asıl Yazarlar: Korneva, A., Zilberberg, L., Rifkin, D.B., Humphrey, J.D., Bellini, C.
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: 2018
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC6367053/
https://ncbi.nlm.nih.gov/pubmed/30306291
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s10237-018-1080-1
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