Effect of ivacaftor on mucociliary clearance and clinical outcomes in cystic fibrosis patients with G551D-CFTR

BACKGROUND. The ability to restore cystic fibrosis transmembrane regulator (CFTR) function with effective small molecule modulators in patients with cystic fibrosis provides an opportunity to study relationships between CFTR ion channel function, organ level physiology, and clinical outcomes. METHOD...

Descripció completa

Guardat en:
Dades bibliogràfiques
Publicat a:JCI Insight
Autors principals: Donaldson, Scott H., Laube, Beth L., Corcoran, Timothy E., Bhambhvani, Pradeep, Zeman, Kirby, Ceppe, Agathe, Zeitlin, Pamela L., Mogayzel, Peter J., Boyle, Michael, Locke, Landon W., Myerburg, Michael M., Pilewski, Joseph M., Flanagan, Brian, Rowe, Steven M., Bennett, William D.
Format: Artigo
Idioma:Inglês
Publicat: American Society for Clinical Investigation 2018
Matèries:
Research Article
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6338313/
https://ncbi.nlm.nih.gov/pubmed/30568035
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1172/jci.insight.122695
Etiquetes: Afegir etiqueta
Sense etiquetes, Sigues el primer a etiquetar aquest registre!

Ítems similars