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Recurrent Encephalopathy with Spinal Cord Involvement: An Atypical Manifestation of Aicardi–Goutières Syndrome

Aicardi–Goutières syndrome (AGS) is a rare, genetic inflammatory disease due to mutations in any of the seven genes discovered to date (TREX1, RNASEH2A, RNASEH2B, RNASEH2C, SAMHD1, ADAR, and IFIH1). Clinical onset is seen most commonly in utero or in infancy; irritability, feeding difficulties, jitt...

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Detalhes bibliográficos
Publicado no:Ann Indian Acad Neurol
Main Authors: Samanta, Debopam, Ramakrishnaiah, Raghu
Formato: Artigo
Idioma:Inglês
Publicado em: Medknow Publications & Media Pvt Ltd 2019
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6327704/
https://ncbi.nlm.nih.gov/pubmed/30692772
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4103/aian.AIAN_12_18
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