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Macrocytic Anemia In Lesch-Nyhan Disease and its Variants

PURPOSE: Lesch-Nyhan disease (LND) is an inherited metabolic disorder characterized by overproduction of uric acid and neurobehavioral abnormalities. The purpose of this study is to describe macrocytic erythrocytes as another common aspect of the phenotype. METHODS: Results of 257 complete blood cou...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:Genet Med
Egile Nagusiak: Cakmakli, Hasan F., Torres, Rosa J., Menendez, Araceli, Yalcin-Cakmakli, Gul, Porter, Christopher C., Puig, Juan Garcia, Jinnah, H.A.
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: 2018
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC6281870/
https://ncbi.nlm.nih.gov/pubmed/29875418
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s41436-018-0053-1
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