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Label-Free Quantitative Proteomics in a Methylmalonyl-CoA Mutase-Silenced Neuroblastoma Cell Line

Methylmalonic acidemias (MMAs) are inborn errors of metabolism due to the deficient activity of methylmalonyl-CoA mutase (MUT). MUT catalyzes the formation of succinyl-CoA from methylmalonyl-CoA, produced from propionyl-CoA catabolism and derived from odd chain fatty acids β-oxidation, cholesterol,...

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Dettagli Bibliografici
Pubblicato in:Int J Mol Sci
Autori principali: Costanzo, Michele, Cevenini, Armando, Marchese, Emanuela, Imperlini, Esther, Raia, Maddalena, Del Vecchio, Luigi, Caterino, Marianna, Ruoppolo, Margherita
Natura: Artigo
Lingua:Inglês
Pubblicazione: MDPI 2018
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6275031/
https://ncbi.nlm.nih.gov/pubmed/30428564
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms19113580
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