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Primary structure and activity of mouse methylmalonyl-CoA mutase.

Methylmalonyl-CoA mutase (MCM) is an adenosylcobalamin-dependent enzyme that catalyses isomerization between methylmalonyl-CoA and succinyl-CoA (3-carboxypropionyl-CoA). Genetic deficiency of this enzyme in man causes an often fatal disorder of organic acid metabolism termed mut methylmalonicacidaem...

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Detalhes bibliográficos
Main Authors: Wilkemeyer, M F, Crane, A M, Ledley, F D
Formato: Artigo
Idioma:Inglês
Publicado em: 1990
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC1149575/
https://ncbi.nlm.nih.gov/pubmed/1978672
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