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Loss of hierarchical imprinting regulation at the Prader–Willi/Angelman syndrome locus in human iPSCs

The human chr15q11-q13 imprinted cluster is linked to several disorders, including Prader–Willi (PWS) and Angelman (AS) syndromes. Recently, disease modeling approaches based on induced pluripotent stem cells (iPSCs) have been used to study these syndromes. A concern regarding the use of these cells...

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Dettagli Bibliografici
Pubblicato in:Hum Mol Genet
Autori principali: Pólvora-Brandão, Duarte, Joaquim, Mariana, Godinho, Inês, Aprile, Domenico, Álvaro, Ana Rita, Onofre, Isabel, Raposo, Ana Cláudia, Pereira de Almeida, Luís, Duarte, Sofia T, da Rocha, Simão T
Natura: Artigo
Lingua:Inglês
Pubblicazione: Oxford University Press 2018
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6240739/
https://ncbi.nlm.nih.gov/pubmed/30102380
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/hmg/ddy274
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