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The Pathogenesis and Therapies of Striated Muscle Laminopathies

Emery-Dreifuss muscular dystrophy (EDMD) is a genetic condition characterized by early contractures, skeletal muscle weakness, and cardiomyopathy. During the last 20 years, various genetic approaches led to the identification of causal genes of EDMD and related disorders, all encoding nuclear envelo...

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Publicado en:Front Physiol
Autores principales: Brull, Astrid, Morales Rodriguez, Blanca, Bonne, Gisèle, Muchir, Antoine, Bertrand, Anne T.
Formato: Artigo
Lenguaje:Inglês
Publicado: Frontiers Media S.A. 2018
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC6218675/
https://ncbi.nlm.nih.gov/pubmed/30425656
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fphys.2018.01533
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