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The Pathogenesis and Therapies of Striated Muscle Laminopathies

Emery-Dreifuss muscular dystrophy (EDMD) is a genetic condition characterized by early contractures, skeletal muscle weakness, and cardiomyopathy. During the last 20 years, various genetic approaches led to the identification of causal genes of EDMD and related disorders, all encoding nuclear envelo...

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Dettagli Bibliografici
Pubblicato in:Front Physiol
Autori principali: Brull, Astrid, Morales Rodriguez, Blanca, Bonne, Gisèle, Muchir, Antoine, Bertrand, Anne T.
Natura: Artigo
Lingua:Inglês
Pubblicazione: Frontiers Media S.A. 2018
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6218675/
https://ncbi.nlm.nih.gov/pubmed/30425656
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fphys.2018.01533
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