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Characterization and outcomes of pulmonary alveolar proteinosis in Brazil: a case series

OBJECTIVE: Pulmonary alveolar proteinosis (PAP) is a rare disease, characterized by the alveolar accumulation of surfactant, which is composed of proteins and lipids. PAP is caused by a deficit of macrophage activity, for which the main treatment is whole-lung lavage (WLL). We report the experience...

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Publicado en:J Bras Pneumol
Main Authors: de Athayde, Rodolfo Augusto Bacelar, Arimura, Fábio Eiji, Kairalla, Ronaldo Adib, Carvalho, Carlos Roberto Ribeiro, Baldi, Bruno Guedes
Formato: Artigo
Idioma:Inglês
Publicado: Sociedade Brasileira de Pneumologia e Tisiologia 2018
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC6188683/
https://ncbi.nlm.nih.gov/pubmed/30043890
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1590/S1806-37562017000000168
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