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Pulmonary alveolar proteinosis in children: a case series

Pulmonary alveolar proteinosis, (PAP) is a rare disease of unknown etiology, characterized by accumulation of intraalveolar proteinaceous material which is rich in lipid and positive on periodic acid-Schiff stain. Two clinically different pediatric types have been defined as congenital PAP which is...

Ausführliche Beschreibung

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Bibliographische Detailangaben
Hauptverfasser: Tabatabaei, Seyyed Ahmad, Karimi, Abdollah, Tabatabaei, Sedigheh Rafiee, Radpay, Badiozzaman, Jadali, Farzaneh, Shiva, Farideh, Jahromy, Mana Hadipour
Format: Artigo
Sprache:Inglês
Veröffentlicht: Medknow Publications 2010
Schlagworte:
Online Zugang:https://ncbi.nlm.nih.gov/pmc/articles/PMC3082791/
https://ncbi.nlm.nih.gov/pubmed/21526069
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