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FUS interacts with ATP synthase beta subunit and induces mitochondrial unfolded protein response in cellular and animal models

FUS (fused in sarcoma) proteinopathy is a group of neurodegenerative diseases characterized by the formation of inclusion bodies containing the FUS protein, including frontotemporal lobar degeneration and amyotrophic lateral sclerosis. Previous studies show that mitochondrial damage is an important...

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Publicat a:Proc Natl Acad Sci U S A
Autors principals: Deng, Jianwen, Wang, Peng, Chen, Xiaoping, Cheng, Haipeng, Liu, Jianghong, Fushimi, Kazuo, Zhu, Li, Wu, Jane Y.
Format: Artigo
Idioma:Inglês
Publicat: National Academy of Sciences 2018
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6187197/
https://ncbi.nlm.nih.gov/pubmed/30249657
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.1806655115
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