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Cardiovascular complications in patients with sickle cell disease

Sickle cell disease (SCD) is an autosomal recessive disease in which homozygosity for a single point mutation in the gene encoding the β-globin chain produces hemoglobin S molecules that polymerize within the erythrocyte during deoxygenation; the result is sustained hemolytic anemia and vaso-occlusi...

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Publicado en:Hematology Am Soc Hematol Educ Program
Autor principal: Gladwin, Mark T.
Formato: Artigo
Lenguaje:Inglês
Publicado: American Society of Hematology 2017
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC6142571/
https://ncbi.nlm.nih.gov/pubmed/29222288
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