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Evolving treatment paradigms in sickle cell disease

Sickle cell disease (SCD) is an inheritable hemoglobinopathy characterized by polymerization of hemoglobin S in red blood cells resulting in chronic hemolytic anemia, vaso-occlusive painful crisis, and multiorgan damage. In SCD, an increased reactive oxygen species (ROS) generation occurs both insid...

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Publicado en:Hematology Am Soc Hematol Educ Program
Main Authors: Jagadeeswaran, Ramasamy, Rivers, Angela
Formato: Artigo
Idioma:Inglês
Publicado: American Society of Hematology 2017
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC6142561/
https://ncbi.nlm.nih.gov/pubmed/29222291
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