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Prevalence and healthcare burden of pulmonary alveolar proteinosis

Pulmonary alveolar proteinosis (PAP) is a rare syndrome of alveolar surfactant accumulation, resulting hypoxemic respiratory failure, and increased infection risk. Despite advances in our understanding of disease pathogenesis and the availability of improved diagnostics, the epidemiology and healthc...

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Detalles Bibliográficos
Publicado en:Orphanet J Rare Dis
Main Authors: McCarthy, Cormac, Avetisyan, Ruzan, Carey, Brenna C., Chalk, Claudia, Trapnell, Bruce C.
Formato: Artigo
Idioma:Inglês
Publicado: BioMed Central 2018
Assuntos:
Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC6069872/
https://ncbi.nlm.nih.gov/pubmed/30064481
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13023-018-0846-y
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