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The Molecular Basis of Pulmonary Alveolar Proteinosis

Pulmonary alveolar proteinosis (PAP) comprises a heterogenous group of diseases characterized by abnormal surfactant accumulation resulting in respiratory insufficiency, and defects in alveolar macrophage- and neutrophil-mediated host defense. Basic, clinical and translational research over the past...

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Autors principals: Carey, Brenna, Trapnell, Bruce C.
Format: Artigo
Idioma:Inglês
Publicat: 2010
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2866141/
https://ncbi.nlm.nih.gov/pubmed/20338813
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.clim.2010.02.017
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