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Antibody inhibition of properdin prevents complement-mediated intravascular and extravascular hemolysis(1)

Paroxysmal nocturnal hemoglobinuria (PNH) is a serious blood disorder characterized by dysregulated complement activation on blood cells. Eculizumab, the current standard therapy and a humanized anti-C5 mAb relieves anemia and thrombosis symptoms of PNH patients by preventing complement-dependent in...

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Dades bibliogràfiques
Publicat a:J Immunol
Autors principals: Gullipalli, Damodar, Zhang, Fengkui, Sato, Sayaka, Ueda, Yoshiyasu, Kimura, Yuko, Golla, Mahdu, Miwa, Takashi, Wang, Jianxiang, Song, Wen-Chao
Format: Artigo
Idioma:Inglês
Publicat: 2018
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6057807/
https://ncbi.nlm.nih.gov/pubmed/29898960
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4049/jimmunol.1800384
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