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Underdeveloped RPE Apical Domain Underlies Lesion Formation in Canine Bestrophinopathies

Canine bestrophinopathy (cBest) is an important translational model for BEST1-associated maculopathies in man that recapitulates the broad spectrum of clinical and molecular disease aspects observed in patients. Both human and canine bestrophinopathies are characterized by focal to multifocal separa...

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Detalles Bibliográficos
Publicado en:Adv Exp Med Biol
Main Authors: Guziewicz, Karina E., McTish, Emily, Dufour, Valerie L., Zorych, Kathryn, Dhingra, Anuradha, Boesze-Battaglia, Kathleen, Aguirre, Gustavo D.
Formato: Artigo
Idioma:Inglês
Publicado: 2018
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC6035728/
https://ncbi.nlm.nih.gov/pubmed/29721958
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/978-3-319-75402-4_38
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