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Severe renal Fanconi and management strategies in Arthrogryposis-Renal dysfunction-Cholestasis syndrome: a case report

BACKGROUND: Arthrogryposis-Renal dysfunction-Cholestasis syndrome (ARC, MIM#208085) is a rare multisystem disease due to mutations in the VPS33B and VIPAR genes, both involved in maintaining apical-basolateral cell polarity. The correlation between mutations and phenotype in the ARC Syndrome is not...

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Detalhes bibliográficos
Publicado no:BMC Nephrol
Main Authors: Rosales, Alejandra, Mhibik, Maissa, Gissen, Paul, Segarra, Oscar, Redecillas, Susana, Ariceta, Gema
Formato: Artigo
Idioma:Inglês
Publicado em: BioMed Central 2018
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6003143/
https://ncbi.nlm.nih.gov/pubmed/29907094
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s12882-018-0926-1
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