A carregar...

Laminin-521 Protein Therapy for Glomerular Basement Membrane and Podocyte Abnormalities in a Model of Pierson Syndrome

Background Laminin α5β2γ1 (LM-521) is a major component of the GBM. Mutations in LAMB2 that prevent LM-521 synthesis and/or secretion cause Pierson syndrome, a rare congenital nephrotic syndrome with diffuse mesangial sclerosis and ocular and neurologic defects. Because the GBM is uniquely accessibl...

ver descrição completa

Na minha lista:
Detalhes bibliográficos
Publicado no:J Am Soc Nephrol
Main Authors: Lin, Meei-Hua, Miller, Joseph B., Kikkawa, Yamato, Suleiman, Hani Y., Tryggvason, Karl, Hodges, Bradley L., Miner, Jeffrey H.
Formato: Artigo
Idioma:Inglês
Publicado em: American Society of Nephrology 2018
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5967757/
https://ncbi.nlm.nih.gov/pubmed/29472414
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1681/ASN.2017060690
Tags: Adicionar Tag
Sem tags, seja o primeiro a adicionar uma tag!