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Biomarkers of Myocardial Fibrosis: Revealing the Natural History of Fibrogenesis in Fabry Disease Cardiomyopathy

BACKGROUND: Cardiomyopathy is a major determinant of overall Fabry disease (FD) prognosis, with the worst outcomes in patients with myocardial fibrosis. Late gadolinium enhancement is currently the gold standard for evaluation of replacement myocardial fibrosis; however, this event is irreversible,...

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Pubblicato in:J Am Heart Assoc
Autori principali: Aguiar, Patrício, Azevedo, Olga, Pinto, Rui, Marino, Jacira, Cardoso, Carlos, Sousa, Nuno, Cunha, Damião, Hughes, Derralynn, Ducla Soares, José Luís
Natura: Artigo
Lingua:Inglês
Pubblicazione: John Wiley and Sons Inc. 2018
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5907540/
https://ncbi.nlm.nih.gov/pubmed/29535138
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1161/JAHA.117.007124
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