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Pretreatment rate of decay in forced vital capacity predicts long-term response to pirfenidone in patients with idiopathic pulmonary fibrosis

Pirfenidone reduces functional decline in patients with Idiopathic Pulmonary Fibrosis (IPF). However, response to treatment is highly heterogeneous. We sought to evaluate whether response to pirfenidone is influenced by the pretreatment rate of forced vital capacity (FVC) decline. Fifty-six IPF pati...

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Detaylı Bibliyografya
Yayımlandı:Sci Rep
Asıl Yazarlar: Biondini, Davide, Balestro, Elisabetta, Lacedonia, Donato, Cerri, Stefania, Milaneschi, Rosanna, Luppi, Fabrizio, Cocconcelli, Elisabetta, Bazzan, Erica, Clini, Enrico, Foschino Barbaro, Maria Pia, Gregori, Dario, Cosio, Manuel G, Saetta, Marina, Spagnolo, Paolo
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: Nature Publishing Group UK 2018
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC5899162/
https://ncbi.nlm.nih.gov/pubmed/29654244
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s41598-018-24303-4
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