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Pretreatment rate of decay in forced vital capacity predicts long-term response to pirfenidone in patients with idiopathic pulmonary fibrosis

Pirfenidone reduces functional decline in patients with Idiopathic Pulmonary Fibrosis (IPF). However, response to treatment is highly heterogeneous. We sought to evaluate whether response to pirfenidone is influenced by the pretreatment rate of forced vital capacity (FVC) decline. Fifty-six IPF pati...

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Dettagli Bibliografici
Pubblicato in:Sci Rep
Autori principali: Biondini, Davide, Balestro, Elisabetta, Lacedonia, Donato, Cerri, Stefania, Milaneschi, Rosanna, Luppi, Fabrizio, Cocconcelli, Elisabetta, Bazzan, Erica, Clini, Enrico, Foschino Barbaro, Maria Pia, Gregori, Dario, Cosio, Manuel G, Saetta, Marina, Spagnolo, Paolo
Natura: Artigo
Lingua:Inglês
Pubblicazione: Nature Publishing Group UK 2018
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5899162/
https://ncbi.nlm.nih.gov/pubmed/29654244
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s41598-018-24303-4
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